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International consensus on the diagnosis and management of pediatric patients with hereditary angioedema with C1 inhibitor deficiency

作者:H. Farkas, I. Martínez-Saguer, K. Bork, T. Bowen, T. Craig, M. Frank, A. Germenis, A. Grumach, A. Luczay, L. Varga, A. Zanichelli, W. Aberer, S. Andrejević, Emel Aygoeren‐Pürsün, A. Banerji, N. Bara, M. Baş, J. Bernstein, S. Betschel, J. Björkander, I. Boccon-Gibod, L. Bouillet, M. Bova, H. Boysen, M. Branco-Ferreira, A. Bygum, T. Caballero, M. Cancian, A. Castaldo, S. Christiansen, M. Cicardi, C. Drouet, J. Fabiani, M. Gompels, M. Gonzalez-Quevedo, J. Gooi, R. Gower, Nihal Mete Gökmen, V. Grivcheva-Panovska, M. Guilarte, O. Gülbahar, E. Hack, R. Hakl, G. Harmat, Miloš Jeseňák, S. Jolles, A. Kaplan, C. Katelaris, M. Košnik, K. V. Kőhalmi, I. Leibovich, M. Levi, Henry H. Li, H. Longhurst, W. Lumry, M. Magerl, A. Malbrán, Ludovic Martin, M. Maurer, E. Mihály, D. Moldovan, M. Murdjeva, Imola Nagy, E. W. Nielsen, Sandra Nieto, P. Nordenfelt, Kristine Obtulowitzc, M. Pedrosa, G. Porębski, N. Prior, A. Reshef, M. Riedl, B. Rosenkranz, P. Schmid‐Grendelmeier, Spath Péter, M. Speletas, M. Staevska, M. Stobiecki, M. Triggiani, N. Veszeli, W. Wuillemin, Z. Xiang, B. Yamamoto, B. Zuraw · 发表于:Allergy. European Journal of Allergy and Clinical Immunology · 年份:2016 · DOI:10.1111/all.13001 · 被引用次数:186 · 研究领域:Medicine

The consensus documents published to date on hereditary angioedema with C1 inhibitor deficiency (C1‐INH‐HAE) have focused on adult patients. Many of the previous recommendations have not been adapted to pediatric patients. We intended to produce consensus recommendations for the diagnosis and management of pediatric patients with C1‐INH‐HAE.