Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration

作者：Paolo Grumati, Luisa Coletto, Patrizia Sabatelli, Matilde Cescon, Alessia Angelin, Enrico Bertaggia, Bert Blaauw, Anna Urciuolo, Tania Tiepolo, Luciano Merlini, Nadir M. Maraldi, Paolo Bernardi, Marco Sandri, Paolo Bonaldo · 发表于：Nature Medicine · 年份：2010 · DOI：10.1038/nm.2247 · 被引用次数：543 · 研究领域：Muscle Physiology and Disorders、Autophagy in Disease and Therapy、Electrospun Nanofibers in Biomedical Applications